In 1921, Dandy discussed the clinical diagnosis and treatment of hydrocephalus secondary to occlusion of the foramina of Magendie and Luschka. In 1944, Walker reported a case of congenital atresia of the outlets of the fourth ventricle treated surgically. Since a de study of this disease entity by Benda in 1954, the condition has commonly been, known by the term, the Dandy-Walker, syndrome. In 1968, Raimondi and et al refered this condition as the DandyWalker cyst.
There is considerable discussion as to the nature of the fundamental embryologic error in this condition, but Benda suggested that atresia of developing fourth ventricular fora Gina was only a part of the syndrome and not its cause, because in some cases reported, the foramina were found to be patent. These patients show characteristic clinical ;symptoms, signs and rac logical findings and should suggest the correct diagnosis. This syndrome was one of the first_cause of hydrocephalus to be treated successfully by surgery.
We are reporting one case of this cyot encountered recently at Yonsei University Medical Center.
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